Результаты исследований: Научные публикации в периодических изданиях › статья › Рецензирование
Human iPSC line was generated from patient-specific adipose tissue-derived mesenchymal multipotent stromal cells carrying two mutations in plakophilin-2 (PKP2) gene using non-integrative reprogramming method. Reprogramming factors OCT4, KLF4, SOX2, CMYC were delivered using Sendai viruses. Pluripotency was confirmed in vitro using immunofluorescence and RT-PCR analysis and in vivo by teratoma assay. The reported iPSC line could be useful tool for in vitro modeling of arrhythmogenic right ventricular cardiomyopathy.
Язык оригинала | английский |
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Страницы (с-по) | 85-88 |
Число страниц | 4 |
Журнал | Stem Cell Research |
Том | 24 |
DOI | |
Состояние | Опубликовано - 1 окт 2017 |
ID: 35806955